What is the treatment of Dandy Walker Syndrome?

Treatment for individuals with Dandy-Walker Syndrome generally consists of treating the associated problems, if needed.

Vasudha Bhat
Other DiseasesWritten by: Vasudha BhatPublished at: Aug 20, 2014Updated at: Aug 20, 2014
What is the treatment of Dandy Walker Syndrome?

What is Dandy-Walker Syndrome?

Dandy-Walker syndrome involves a congenital brain malformation of the cerebellum and the fluid-filled spaces around it. Cerebellum is an area at the back of the brain that controls movement.
The cause for this syndrome is unknown in most cases while in others it is known to have resulted from autosomal recessive genes, meaning, getting an abnormal gene on one of the autosomal chromosomes from each parent.

Dandy-Walker Syndrome Treatment

Treatment for Dandy-Walker Syndrome

The treatment for Dandy-Walker syndrome usually consists of treating the problem associated with the syndrome, if required. A surgical procedure which is called a shunt may be needed to drain off the extra fluid from the brain. This will help is lessening the intracranial pressure and prevent swelling. The parents of children suffering from Dandy-Walker syndrome can also benefit from the genetic counseling if they are aiming at having more children.

Symptoms of Dandy-Walker Syndrome

The symptoms of Dandy-Walker syndrome are usually seen in early infancy stage and can include the following:

  • slow motor development
  • progressive enlargement of the skull.

Dandy-Walker Syndrome Treatment

In older children, symptoms of increased intracranial pressure include:

  • irritability
  • vomiting
  • convulsions
  • signs of cerebellar dysfunction, such as unsteadiness, lack of muscle
  • co-ordination, or jerky movements of the eyes
  • increased head circumference
  • bulging at the back of the skull
  • problems with the nerves that control the eyes, face and neck
  • abnormal breathing patterns
  • seizures (up to 15%).

Image courtesy: Getty Images

Read more on Dandy-Walker Syndrome.