Hydranencephaly is a condition in which the brain's cerebral hemispheres are absent to varying degrees and the remaining cranial cavity is filled with cerebrospinal fluid. An infant with hydranencephaly may appear normal at birth. The infant's head size and spontaneous reflexes such as sucking, swallowing, crying, and moving the arms and legs may all seem normal. However, after a few weeks the infant usually becomes irritable and has increased muscle tone.
Prognosis of Hydranencephaly
The 'prognosis' of Hydranencephaly usually refers to the likely outcome of Hydranencephaly. The prognosis may include the duration of the disease, its chances of complications, probable outcomes, prospects for recovery, recovery period, survival rates, and death rates.
The outlook for children with hydranencephaly is generally poor, and many children with this disorder die before age 1. However, in rare cases, children with hydranencephaly may survive for several years or more.
Medical text identifies that hydranencephalic children simply have only their brain stem function remaining thus leaving formal treatment options as symptomatic and supportive. Severe hydrocephalus causing macrocephaly, a larger than average head circumference, can easily be managed by placement of a shunt and oftentimes displays a misdiagnosis of another lesser variation of cephalic condition. Plagiocephaly, the asymmetrical distortion of the skull, is another typical associated condition that is easily managed through positioning and strengthening exercises to prevent torticollis, a constant spasm or extreme tightening of the neck muscles.
Though medical research exclusive to hydranencephaly is limited, there are research efforts in the realm of neural tube defects and prevention of congenital neurological conditions. We encourage you to research all aspects of the condition prior to settling on one aspect of the diagnosis.
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