What is the Prognosis of Gerstmann Straussler Scheinker Disease?

By  ,  Onlymyhealth editorial team
Sep 04, 2014

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Quick Bites

  • GSS is a neurodegenerative disorder of brain.
  • It can only be inherited and can be found in few families.
  • It leads to ataxia which progresses slowly.
  • The disorder leads to eventual death of the patient.

What is Gerstmann-Straussler-Scheinker disease (GSS)?

Gerstmann-Straussler-Scheinker disease (GSS) is a rare condition and neurodegenerative disorder of the brain. In almost all cases it is being inherited and can be found only in few families around the world. The symptoms of the disease usually start occurring between the age of 35 and 55. Suring early stages the patients experience varied levels of lack of muscle coordination or ataxia, including clumsiness, unsteadiness and problem in walking. As the diseases progresses, ataxia becomes more significant and most patient suffer from dementia. Other symptoms of the disease include dysartria, nystagmu, spasticity and visual disturbances at times which can lead to blindness. Some patients may also suffer from deafness and in some cases parkinsons features are also present.

Gerstmann-Straussler-Scheinker disease Prognosis

What is the Prognosis?

GSS is a slowly progressing disease which usually lasts from 2-10 years. This disease can cause severe disabilities and eventual death. The patient goes into a coma or has a secondary infection such as aspiration pneumonia due to an impaired ability to swallow.

Gerstmann-Straussler-Scheinker disease Prognosis

What is the Treatment?

There is no cure for GSS. There is no known treatment for slow progression of the diseases also. The recent therapies are can relieve the symptoms and can make the patient comfortable.

Image courtesy: Getty Images

Read more on Gerstmann-Straussler-Scheinker Diagnosis and Prognosis.

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